What do you feed a newborn with galactosemia?
A child on a galactose-restricted diet can eat most foods containing protein, such as beef, poultry and eggs. They can also eat most types of fruits, vegetables, and grains. Since children with galactosemia cannot consume milk products, their calcium levels may be too low.
Why should children avoid milk with galactosemia?
Galactose is half of the chemical lactose, which is most common in milk. Babies and children with galactosemia need to avoid eating or drinking anything that has milk in it, whether from breastfeeding or from an animal. If they get too much galactose, it may damage their liver, kidneys, eyes, or brain.
Is galactosemia a contraindication to breastfeeding?
Breast feeding is contraindicated 1) for infants with phenylketonuria, rare amino acidurias, and galactosemia; 2) for infants whose mothers have diseases such as infectious tuberculosis and venereal disease; and 3) for infants whose mothers are taking medications which might be harmful to the infant.
Is galactose found in breast milk?
Galactosemia means “galactose in the blood”. Babies with this metabolic condition are not able to metabolize a certain type of sugar (galactose) found primarily in breast milk, cow’s milk, and dairy products. When galactose can’t be broken down and digested, it builds up in the tissues and blood in large amounts.
What happens if a baby has galactosemia?
People with galactosemia are unable to fully break down the simple sugar galactose. Galactose makes up one half of lactose, the sugar found in milk. If an infant with galactosemia is given milk, substances made from galactose build up in the infant’s system. These substances damage the liver, brain, kidneys, and eyes.
How do you know if your baby has galactosemia?
Symptoms start to show up within a few days after they begin to drink breast milk or formula with lactose — the milk sugar that contains galactose. Your baby first loses their appetite and starts vomiting. Then they get jaundice, a yellowing of the skin and the whites of their eyes. Diarrhea is common, too.
What is the life expectancy of someone with galactosemia?
With a galactose-restricted diet patients have a normal life expectancy. However, patients may still suffer long-term complications such as problems of mental development, disorders of speech, hypergonadotrophic hypogonadism and decreased bone mineral density (Bosch 2006).
Is there a cure for galactosemia?
There is no cure for galactosemia or approved medication to replace the enzymes. Although a low-galactose diet can prevent or reduce the risk of some complications, it may not stop all of them.
Can a baby with PKU breastfeed?
Can I breastfeed my baby if I have PKU? Yes you can breastfeed! Breastfeeding is possible for women who have normal babies and who have phe levels in the safe range.
When can a mother not breastfeed her baby?
How long should a mother breastfeed? The American Academy of Pediatrics recommends that infants be exclusively breastfed for about the first 6 months with continued breastfeeding along with introducing appropriate complementary foods for 1 year or longer.